T. Leguyadec et al., MULTIPLE TRICHODISCOMAS ASSOCIATED WITH INTESTINAL POLYPOSIS, Annales de dermatologie et de venereologie, 125(10), 1998, pp. 717-719
Background. Trichodiscoma is an uncommon benign tumor of the pilosebac
eous system. Case report. An 83-year-old man had a past history of ade
nomatous polyps of the colon. The subject's brother had died from canc
er of the colon. Over the past 4 years, the patient had developed appr
oximately 30 small asymptomatic papulonodular tumors on the trunk. Ski
n biopsy demonstrated trichodiscomas. Discussion. Together with fibrof
olliculomas and perifollicular fibromas, trichodiscomas are benign tum
ors of the pilosebaceous system. These different rumors may occur simu
ltaneously as in Birt-Hogg-Dube syndrome which associates trichodiscom
a and familial colonic polyposis. This combination has only been repor
ted in Birt-Hogg-Dube syndrome or with perifollicular fibromas. Conclu
sion. This case suggests that patients with hamartomas of the piloseba
ceous system should undergo explorations in search for digestive tract
polyposis.