CONGENITAL MEGALOURETHRA ASSOCIATED WITH URETHRAL DUPLICATION AND IMPERFORATE ANUS

A newborn with a prenatal diagnosis of right hydroureteronephrosis and enlarged penis is presented. At birth, the baby had an imperforate an us (IA) with a megalourethra; radiologic and ultrasonographic studies showed left polycystic kidney and right hydroureteronephrosis, right v esico-ureteral. reflux, and an incomplete urethral duplication with di latation of the posterior urethra. The IA was corrected on the Ist day of life and a vesicostomy was performed at 1 month. At 1 year of age the valve obstructing the ventral posterior urethra was resected and t he vesicostomy was closed. At 14 months the baby underwent a urethropl asty with a vertical preputial tubularized island flap and excision of the penile urethral duplication. Exact knowledge of the malformation was essential in planning the appropriate surgical treatment.