HYPERTENSION SECONDARY TO PROGRESSIVE VASCULAR NEUROFIBROMATOSIS

A 4 year old girl with neurofibromatosis type 1 (NF1) was referred for hypertension. An aortogram showed narrowing of the left main renal ar tery. An angiogram three and a half years later showed coarctation of the abdominal aorta. She underwent aortoplasty but the stenosis recurr ed. Vascular involvement in NF1 may be progressive and requires long t erm follow up.