Bilateral epidural hematoma in a pyknodysostotic child

Pyknodysostosis is a rarely encountered disease. It is characterized by abn ormal facial development, fragility of the bones with relatively mild traum a, cranial abnormalities including widely opened sutures and fontanels fron tal bossing, wrinkled skin, finger and nail abnormalities. In the literatur e, pyknodysostosis was reported only as case reports. Here, we describe a p yknodysostotic child with a bilateral parietal epidural hematoma, caused by a relatively mild head trauma, He was operated on, and the hematoma was ev acuated through two different parietal craniotomies, We reported this case, since pyknodysostosis is a rare disease, and our case is the first one who had a surgical intervention as well as being the first with an epidural he matoma in pyknodysostosis.