A. Adil et al., Lymphangioma and lymphangiomatosis: the contribution of imaging studies. Areview of ten cases., SEM HOP PAR, 75(11-12), 1999, pp. 319-325
Cystic lymphangioma is a congenital neoplasm seen in children and young adu
lts. Means of achieving the diagnosis are reviewed with reference to ten ca
ses. Nine patients had a localized lesion involving the orbit (n=1), neck (
n=1), mediastinum (n=2), neck and mediastinum (n=1), pancreas (n=2), mesent
ery (n=1), or spleen (n=1). The remaining patient had diffuse involvement o
f the mediastinum, thoracic and abdominal wall, retroperitoneum, and mesent
ery. Based on these ten cases and on previously published data, the clinico
pathologic characteristics of these lesions are reviewed and the contributi
on of imaging studies to the diagnosis is discussed. Computed tomography (C
T) and magnetic resonance imaging (MRI) show both the monomorphic and polym
orphic forms of cystic lymphangioma. MRI is particularly valuable for deter
mining the extent of the lesion, especially as some of these tumors infiltr
ate neighboring tissues. Aspiration under ultrasound or CT guidance, if pos
itive, adds considerably to the diagnosis of cystic lymphangioma.