Neurocutaneous melanosis presenting with intracranial amelanotic melanoma

We describe imaging findings in a 2-year-old girl,vith neurocutaneous melan osis and malignant cerebral melanoma. Because the cerebral melanoma in this child was of the amelanotic type, high-signal intensity on unenhanced T1-w eighted images was not present. The cutaneous lesions played a crucial role in establishing a correct (presumed) histopathologic diagnosis on the basi s of the imaging findings. To our knowledge this is the first report descri bing an intracranial amelanotic malignant melanoma in association with neur ocutaneous melanosis.