A unique case of initially right sided varicella tester induced Ramsay-Hunt
syndrome with complete vestibular loss is reported. The patient subsequent
ly developed deficits of the left vestibule 5 months later. An autoimmune p
athogenesis of the left vestibular failure rather than bilateral varicella
tester infection was suggested by the following data: (1) no evidence of ve
sicular eruptions on the left auricle and the virtual absence of antiviral
antibodies after onset of bilateral vestibulopathy; (2) prompt response of
the left vestibule to immmunosuppressive therapy with corticosteroids; and
(3) presence of atypical nervous tissue specific autoantibodies against a 4
5 kDa protein.