Background/Purpose: Purpura fulminans (PF) is a serious, often life-threate
ning disease. As more chilren are surviving their disease, surgeons are pre
sented with increasing numbers of multiple and complicated wounds as sequel
ae of PF. The purpose of this paper is to review the management of nine cas
es of PF, and present the reconstruction method in treating bilateral expos
ed elbow and knee joints.
Methods: All cases of pediatric patients with PF and treated by the divisio
n of plastic and reconstructive surgery between 1986 and 1998 were reviewed
.
Results: Seven children (78%) had meningococcal PF, and one (11%) had PF af
ter Haemophilus influenza septicemia. PF developed in one (11%) but with no
growth in either blood or cerebrospinal fluid cultures, Five children (56%
) required amputation procedures. Two children (22%) required knee disartic
ulation. Two patients (22%) had free myocutaneous flap transfers for bone c
overage. One (11%) had PF involving the face.
Conclusions: Meningococcal PF is a rare, often life-threatening disease gen
erally of childhood. More children are surviving their diseases but with de
vastating sequelae. Successful reconstructive treatment outcome of these ch
ildren requires a multidisciplinary team approach involving multiple specia
lties. The goal is to preserve function, maintain maximal length, and salva
ge limbs when possible. Flexibility and innovation are necessary in treatin
g these multiple and complicated wounds. Copyright (C) 1999 by W.B. Saunder
s Company.