External respiration function in adults and children with anomalous heart chordae

Aim. To compare respiratory function in adults and children whose heart cho rdae were in anomalous position (AC) with reference to severity of heart co nnective tissue dysplasia syndrome. Materials and methods. The study included ninety one 6-14-year-olds and 125 adults with AC. The patients were divided into groups by the degree of atr ioventricular valvular prolapse (AVVP). External respiration function was e xamined, and the loop flow-volume was registered by the pulmonological comp uter system. Inhalation bronchospasmolytic test with berotec was performed Results. Tracheobronchial dyskinesia related in degree to AVVP severity was found in 76 and 35% of the adults and children with AC and A WP, respectiv ely. The berotec test allowed more precise evaluation of tracheobronchial d yskinesia. Conclusion. Functional insufficiency of the connective tissue in patients w ith cardiac connective tissue dysplasia syndrome progresses with age.