The historical background of solitary and multiple myxoid tumors of the der
mis is accompanied by a confusing conglomeration of names. We report a case
whose histologic features do not fit exactly with previous classifications
. It appeared as a solitary angiomyxoma of the face containing stellate ple
omorphic cells and exhibiting a locally infiltrative behavior with tendency
for recurrences over more than 25 years. This recurrent pleomorphic solita
ry angiomyxoma appears to be distinct from cutaneous myxomas that exhibit a
very low local recurrence rate and from malignant tumors with myxoid depos
its. The treatment consisted of a wide surgical excision.