Recurrence of desmoid tumor in a multivisceral transplant patient with Gardner's syndrome

Background Desmoid tumors are locally invasive fibromatous tumors, which, i n patients with Gardner's syndrome, usually occur in the abdominal wall or intra-abdominally, After excision, they tend to recur, often leading to mul tiple bowel resections, Methods. This is a report of the clinical course of a patient with Gardner' s syndrome and desmoid tumor who had multiple enterectomies and gradually d eveloped short-gut syndrome. He required prolonged parenteral nutrition, wh ich damaged the liver. The patient underwent a multivisceral transplantatio n as a life-saving procedure. Results. After the transplant, the desmoid tumor recurred in the thoracic w all twice and was successfully resected, It also recurred in the abdominal cavity, compressing the intestinal loops; the tumor was excised uneventfull y, leaving the graft intact, The recurrent tumors were all of recipient ori gin, Conclusions. Intestinal and multivisceral transplantation could be consider ed in patients with short-gut syndrome caused by recurrent desmoid tumor. I n the case of posttransplant tumor recurrence, resection is the only option recommended.