Background: Meningiomas originating in the internal auditory meatus ar
e rare and have been reported in only 12 cases. Patient: We report abo
ut another case, which showed primarily the symptoms of sudden hearing
loss and diagnostic signs of an intrameatal acoustic neuroma. The ABR
interpeak latency IV was prolonged. The tumor was detected by MRI sca
n with gadolinium contrast enhancement and resembled the features of a
n intrameatal acoustic neuroma. Results: The tumor was removed via a m
iddle fossa approach with preservation of hearing and facial nerve fun
ction. Histological examination however revealed a meningioma originat
ing from the internal auditory meatus. Conclusions: Contrast enhancing
intrameatal tumors are most often acoustic neuromas. However even des
pite subtile audiological and neurotological examination and sophistic
ated imaging techniques they cannot be differentiated clinically from
meningiomas at this location. Removal of the intrameatal tumor via a m
iddle fossa approach seems to be the best surgical approach to preserv
e hearing and facial nerve function.