Intrapericardial teratomas are rare armors usually occurring in early infan
cy. Such a case was diagnosed in a 20 week old fetus, with a lethal outcome
. About fifteen cases of intrapericardial teratoma have been reported in th
e fetal period. They are usually symptomatic, with a more or less severe pe
ricardial effusion, sometimes complicated by cardiac compression and/or hyd
rops fetalis. Prognosis of the prenatally diagnosed pericardial teratomas i
s mole related to the occurrence of hydrops fetalis than to the behavior of
the tumor itself. The main interest of sonographic ante-natal diagnosis co
nsists of the possible improvement of hemodynamic consequences through in u
tero pericardiocentesis. Macroscopic and microscopic features of this cardi
ac tumor are similar to those of extrapericardial teratomas. Most tumors di
scovered in fetal period are mature and histologically benign lesions. Only
one case showed immature components. The coexistence of a malignant compon
ent (germ cell or non germ cell tumor) has been described in the postnatal
and adulthood.