A 2-year-old girl presented with an anterior sacral meningocele completely
occupied by an epidermoid tumor. Preoperative magnetic resonance imaging ha
d shown the meningocele with contents of the same intensity as cerebrospina
l fluid. Surgery via a posterior sacral approach disclosed the tumor beneat
h an unexpected membrane inside the meningocele. Additionally, the presence
of pus inside epidermoid tumor suggested that possible episodes of asympto
matic meningitis or other infection might have occurred before treatment, t
hese being the major complication in anterior sacral meningocele. Therefore
, we recommend that surgical treatment should be performed at the earliest
possible stage in childhood, once the diagnosis is established, and dural p
lasty carried out to prevent infectious complications.