Feminizing genital reconstruction, sigmoid vaginal replacement and anorectoplasty as a one-stage procedure for anorectal atresia associated with ambiguous genitalia

Anorectal atresia associated with male pseudohermaphroditism presents both diagnostic and surgical challenges. In the past, multiple operations were n ecessary for feminizing genitoplasty in gender-reassigned children with amb iguous genitalia. We combined the repair of an imperforate anus with a femi nizing genitoplasty, including sigmoid vaginal replacement using the poster ior sagittal approach in a 3-months-old infant. We conclude that a primary complete reconstruction is advantageous and should be performed in this con dition.