RIGHT OUTFLOW TRACT OBSTRUCTION BY A PEDUNCULATED NEUROFIBROMA - CASE-REPORT AND LITERATURE-REVIEW

Right outflow tract obstruction due to neurofibroma is rare, with only four cases identified in the world literature. Obstruction due to a p edunculated neurofibroma has never been reported. A 36-year-old woman with no known heart disease presenting with dyspnea, palpitations and chest pain was shown on echocardiogram to have a mobile right ventricu lar mass. Cardiac catheterization revealed normal coronary arteries an d right ventricular outflow tract obstruction by a pedunculated mass, which was surgically removed and histologically proven to be a benign neurofibroma. Following surgery the patient's symptoms disappeared, wi th no recurrence three years postoperatively.