A 34-year-old Japanese woman (gravida 2, para 2) with polyhydramnios and no
n-immunological hydrops fetalis was referred to our department at 32 weeks
of gestation. On admission, the blood pressure was 120/60 mmHg and there wa
s no pitting edema of the lower extremities. An ultrasound examination disc
losed a large placental tumor 5.8 cm x 4.4 cm x 4.8 cm. Fetal lung compress
ion was suspected because the lung-thorax transverse area ratio was 0.13. T
he preload index of the inferior vena cava was 0.74, suggesting fetal cardi
ac failure. After fetal pleural effusion was aspirated, lung compression de
veloped. Cordocentesis was performed at 33 weeks of gestation, and the feta
l karyotype was confirmed to be 46, XY from an umbilical blood cultivation.
The patient underwent a cesarean section at 33 weeks of gestation due to s
evere uterine contraction after preterm FROM. The baby was a 3,840 g male w
ith a distended abdomen. Apgar score at 1 minute was I. A chest X-ray demon
strated respiratory distress syndrome. The baby was discharged on the 69th
day after birth and he is now 2 years and 9 months old and healthy.