The occurrence of sarcoma in a benign cystic teratoma is very rare. We repo
rt the first poorly differentiated, malignant mixed mesodermal tumor with a
component of rhabdomyosarcoma to arise in a benign cystic teratoma of the
ovary. The tumor was staged as FIGO IC due to capsule invasion. Although co
mbination chemotherapy of cisplatin, ifosfamide and mesna, was instituted,
the disease took a rapidly progressive course. After an unusual metastasis
to the scapula was detected, the patient deteriorated and died in the forth
postoperative month. (C) 1999 Elsevier Science Ireland Ltd. All rights res
erved.