Tuberous sclerosis associated with multiple hepatic lipomatous tumors and hemorrhagic renal angiomyolipoma

We report a case of tuberous sclerosis associated with hepatic lipomatous t umors and renal angiomyolipomas. Abdominal ultrasonography revealed a high echoic large tumor in the left kidney. A provisional diagnosis of angiomyol ipomas of the kidney was made based on computed tomography. Subsequent lapa rotomy revealed that the extracted tumor was renal angiomyolipoma. It was a lso revealed that there was an association with hepatic lipomatous tumors t hought to be lipomas or angiomyolipomas by liver biopsy. Nearly half of all cases of angiomyolipoma in the kidney are reported as occasional associati on with tuberous sclerosis complex, but lipomatous tumors in the liver are rare.