Persistence of the right umbilical vein is variably associated with life-th
reatening malformations of the fetal genitourinary, gastrointestinal, cardi
ac, and skeletal systems. Varices of the intraabdominal umbilical vein, alt
hough not necessarily associated with other malformations, do seem to carry
a risk of fetal mortality, especially if they are large or appear early du
ring the pregnancy. We report the prenatal diagnosis of the rare combinatio
n of persistence and varix of the right umbilical vein in an otherwise heal
thy infant. (C) 1999 John Wiley & Sons, Inc.