MR imaging of pachydermoperiostosis

A case of pachydermoperiostosis who demonstrated the whole syndrome (pachyd erma, periostitis, and cutis verticis gyrata) is presented, and the Magneti c Resonance Imaging (MRI) appearances of the long bone and scalp changes ar e demonstrated. MRI of the cruris demonstrated fluffy periosteal new bone f ormation that encroached on the medullary cavity as well as expansion of th e diaphysis. Cranial changes included thickening of the diploe associated w ith diminished signal of the intradiploic fat, and thickening of the scalp with furrowing.