Cardiac rhabdomyomas are benign tumours closely associated with tubero
us sclerosis. We report on a neonate with a cardiac rhabdomyoma, which
simulated tricuspid atresia with duct-depending pulmonary perfusion d
ue to almost complete obliteration of right ventricular cavum. Under i
nfusion of prostaglandin E-1 the newborn stabilized and was successful
ly operated on the 3rd day of life. We conclude that successful tumour
resection is possible in neonates with cardiac rhabdomyomas causing r
elevant hemodynamic obstruction.