Pigmented schwannomas of the spinal canal are rare entities. We present a c
ase of such in an unusual, ventral intradural, extramedullary location in a
27-year-old man, Imaging and histopathologic findings, including electron
microscopy, showed an intradural, extramedullary pigmented schwannoma, dens
ely adherent to the leptomeninges of the anterior median septum. This lesio
n is demonstrative of the neuroectodermal origin of these lesions and repre
sents a rare location of these tumors.