Presacral teratomas are rare tumors derived from more than one embryonic ge
rm layer and are usually diagnosed in infancy. It has been estimated that t
he incidence of presacral teratoma in children ranges from 1 in 30,000 to 1
in 43,000 live births. However, the diagnosis of these tumors in adults is
extremely rare. H. Head et al. reviewed the world literature in 1975 and f
ound only 71 reported cases. Since that time, an additional 14 cases have b
een reported, and only one of these was found in the United States. This st
udy reports a case of an adult male who presented with recurrent infected p
ilonidal cysts that proved to be benign presacral teratoma at biopsy. The p
atient underwent resection by left hemisacrectomy and primary closure using
a posterior approach and, since this procedure, has had no evidence of rec
urrence. The case is presented along with a review of the relevant literatu
re.