A congenital rhabdomyosarcoma presented as a partially necrotic mass on the
left forearm on delivery at term. Ulceration and persistent bleeding were
managed by primary curettage followed by local resection including partial
excision of the muscles of the extensor compartment df the forearm. The def
ect was resurfaced with a split skin graft. The surgery was followed by che
motherapy according to the IVA regime. There was no recurrence at 2 years o
f age and the limb was fully functional. The presentation and management of
rhabdomyosarcoma are discussed.