Behcet's disease is a systemic vasculitis of unknown etiology that pro
gresses by exacerbations followed by partial remissions. The diagnosis
currently rests on international criteria. Aphthous ulcers of the ora
l cavity and genitalia are the hallmarks of the disease. Systemic mani
festations can involve the joints, skin, eyes, nervous system, ad bloo
d vessels. Behcet's disease is rare in children. Two cases of Behcet's
disease with mucocutaneous and ocular symptoms in a girl aged 10 year
s 6 months and a boy aged ten years are reported. Ocular manifestation
s respond incompletely to available treatments and govern the prognosi
s of the disease.