Angiomyolipoma (AML) is a benign mesenchymal tumor predominantly occurring
in the kidney. Despite its low incidence of 0.07-0.3% in an unselected popu
lation, this tumor is well known, because the typical AML can be diagnosed
without histological confirmation by a combination of ultrasound (US) and c
omputerized tomography (CT) imaging in up to 95% of cases. In contrast, sim
ultaneous involvement of the kidney and the regional lymph nodes is less kn
own and might be confused with metastasizing malignant tumor. We report a c
ase of the very uncommon simultaneous involvement of the kidney and the lym
ph nodes in AML.