Unsuccessful surgical treatment of hip dislocation in congenital sensory neuropathy with anhidrosis - A case report

A six-year-old girl with congenital sensory neuropathy with anhidrosis (CSN A) presented with bilateral hip dysplasia and subluxation on the right side . Conservative treatment of the hips by closed reduction and a plaster cast w as unsuccessful. When aged seven years the patient had an intertrochanteric varus rotation osteotomy on the right side, but subluxation was again evid ent after five months. A Sailer-type pelvic osteotomy was carried out follo wed by immobilisation, but one year later subluxation was present in the ri ght hip and dislocation in the left. At the age of nine years, the right fe moral head. resembled a Charcot-joint, although walking ability was preserv ed. In patients with CSNA, surgery may not always be advisable.