C. De Felice et al., Congenital cystic adenomatoid malformation of the lung associated with esophageal atresia and tracheoesophageal fistula, PEDIAT SURG, 15(3-4), 1999, pp. 260-263
Bronchopulmonary malformations associated with esophageal atresia (EA) and
tracheoesophageal fistula (TEF) are extremely rare. The authors describe a
case-of type II congenital cystic adenomatoid malformation (CCAM) of the ri
ght lower lobe associated with EA and TEF(Vogt-Gross type C) in a full-term
female infant. The CCAM presented as an incidental radiologic finding, and
a contralateral tension pneumothorax developed shortly after surgical repa
ir of the EA. Early recognition of this rare association is essential for c
orrect operative management.