Dentin dysplasia, type II - Report of 2 new families and review of the literature

Dentin dysplasia, type II, is an inherited autosomal dominant disorder in w hich primary teeth are amber and translucent, with pulp chambers obliterate d by abnormal dentin. The permanent teeth have a normal coronal morphologic character and coloration but exhibit "thistle tube"-shaped pulp chambers a s well as numerous pulpal calcifications. The disorder has traditionally be en thought to be somewhat rare; however, this article presents 2 new famili es in which several generations with the disorder were reported to the auth ors within a 1-year period. It also includes a review of the literature doc umenting a total of 17 previously reported families.