Blue rubber bleb nevus (Bean syndrome): Evolution of four cases and clinical response to pharmacologic agents

Authors
Boente, MD Cordisco, MR Frontini, MD Asial, RA
Citation
Md. Boente et al., Blue rubber bleb nevus (Bean syndrome): Evolution of four cases and clinical response to pharmacologic agents, PEDIAT DERM, 16(3), 1999, pp. 222-227
Citations number
26
Categorie Soggetti
Pediatrics
Journal title
PEDIATRIC DERMATOLOGY
ISSN journal
07368046 → ACNP
Volume
16
Issue
3
Year of publication
1999
Pages
222 - 227
Database
ISI
SICI code
0736-8046(199905/06)16:3<222:BRBN(S>2.0.ZU;2-1
Abstract
Blue rubber bleb nevus (BRBN) syndrome is a rare disorder characterized by distinctive cutaneous and gastrointestinal vascular malformations. The latt er may lead to bleeding complications. We followed four affected children f or at least 5 years. The evolution of their disease and the value of pharma cologic agents (steroids, interferon) in the management of some of these pa tients are discussed.