A. Misra et al., Portal hypertension due to extensive hepatic cysts in autosomal dominant polycystic kidney disease, SOUTH MED J, 92(6), 1999, pp. 626-627
Liver cysts are a well-recognized feature of autosomal dominant polycystic
kidney disease (ADPKD) and occur in 77% of patients more than 60 years old.
Serious sequelae, however, are rare, the two most common complications bei
ng pain and cyst infections. Portal hypertension has been reported in ADPKD
due to the rare presence of congenital hepatic fibrosis. We report a case
of ADPKD in a patient who had portal hypertension due to distortion of port
al vein and venules by extensive hepatic cysts.