When the pediatrician went to examine Jenny at 1 day of age in the hospital
, she was not surprised to find a healthy, full-term neonate with a normal
physical examination, including a normal developmental assessment. She was
responsive and robust with wide open eyes that engaged her mother and the p
ediatrician.
A review of the medical records revealed that both parents were significant
ly hearing-impaired. Jenny's mother had a familial form of congenital neuro
sensory deafness. Both maternal grandparents had the same condition. Her mo
ther learned to sign at an early age and completed a college degree. Jenny'
s father acquired his deaf condition at 6 years of age after an episode of
viral encephalitis. He communicated through sign language and was a success
ful administrator.
When the pediatrician suggested a hearing test (brainstem auditory evoked p
otential), Jenny's mother, who was able to use spoken language as well as s
ign language, responded with a soft smile. "I don't think that will be nece
ssary. We will know if she can hear in a short time."