A 7-year-old girl had non-bullous congenital ichthyosiform erythroderma (NB
CIE) in treatment with retinoids. She also suffered continuous desquamation
of the external ears, recurrent external otitis, chronic adenoiditis, tuba
ric dysfunction and intermittent episodes of otitis media and developed a c
holesteatoma in her left ear. Chronic scaling disorders, such as NBCIE and
other ichthyosis, can be entities at risk for the development of cholesteat
oma in childhood. (C) 1999 Elsevier Science Ireland Ltd. All rights reserve
d.