The objective of this study was to assess the long-term results of partial
laryngectomy for benign neural tumors of the larynx. We reviewed 8 patients
with laryngeal involvement - 7 with neurofibromatosis and 1 without - trea
ted between 1980 and 1994. The mean age was 6.5 years. A partial laryngecto
my was performed in 7 cases. All the tumors were located in the aryepiglott
ic folds. Clinical, radiologic, and endoscopic follow-ups were used for eva
luating recurrence. A good laryngeal airway, swallowing without aspiration,
and voice quality were sought in assessing the functional results. Five pa
tients had good functional results witt! no recurrences. One patient died o
f malignant transformation and metastatic dissemination of his disease. To
summarize, partial laryngectomy is a relatively safe and effective procedur
e, even in childhood, for treating this rare localization of neurofibromato
sis. A malignant transformation of the tumor is possible and carries a poor
prognosis.