Perineal reconstruction for severe sequela of ecthyma gangrenosum - Reportof a case

Ecthyma gangrenosum is a cutaneous gangrenous disorder which usually follow s Pseudomona aeruginosa infection and is found mainly in immunosuppressed c hildren. We describe a case of a five-year-old female with leukemia with a severe perineal ecthyma gangrenosum resulting in a cloaca-like deformity. O ne year later a perineoplasty with puborectalis interposition and overlappi ng external anal sphincteroplasty was successfully performed, achieving sat isfactory continence.