Bilateral proptosis: an unusual presentation of fibrous dysplasia

Citation
Ma. Horgan et al., Bilateral proptosis: an unusual presentation of fibrous dysplasia, BR J NEUROS, 13(3), 1999, pp. 335-337
Citations number
7
Categorie Soggetti
Neurology
Journal title
BRITISH JOURNAL OF NEUROSURGERY
ISSN journal
02688697 → ACNP
Volume
13
Issue
3
Year of publication
1999
Pages
335 - 337
Database
ISI
SICI code
0268-8697(199906)13:3<335:BPAUPO>2.0.ZU;2-I
Abstract
Fibrous dysplasia is a benign, developmental bone disorder of unknown aetio logy. With involvement of the facial bones, indications for surgical interv ention include cosmetic deformity and/or progressive neurological dysfuncti on. We present the case of a 36-year-old female with bilateral orbital lesi ons whose initial presentation was that of progressive proptosis and visual loss. She underwent bilateral pterional craniotomies with gross total rese ction of her rumours. Review of the literature reveals several cases of uni lateral orbital fibrous dysplasia. This appears to be the first reported ca se of distinct, bilateral orbital fibrous dysplasia.