A patient, 5 years of age, presented with a swelling on the right side of t
he neck. Ultrasonography and computed tomography confirmed a diagnosis of p
hlebectasia of the right internal jugular vein (IJV). The patient underwent
operation and the dilated IJV was excised. Dilatation of the IJV with a Va
lsalva maneuver suggested a mechanical obstruction in the neck or mediastin
um. However, the exact cause is still unknown. Finally, we found the patien
t to have a thinning of the wall but no other associated abnormality.