Retroperitoneal fibrosis - Ormond's disease

Retroperitoneal fibrosis (RPF) is characterised by proliferation and fibros is of retroperitoneal tissue. This leads to ureteral and pelvic obstruction by fibrotic masses. These structures may infiltrate up to the mediastinum and the pleura. Association with vasculitis and inflammatory rheumatic dise ases can be observerd. MRT is superior to CT in diagnostic requirement. Med ical treatment with tamoxifen and steroids may be effective additional to s urgery. Although the pathogenesis remains unknown RPF seems to be an autoim mune disease. Malignant tumors must be taken in consideration in all cases.