Ehlers-Danlos syndrome: Surgical management of mitral regurgitation and atrial fibrillation

Ehlers-Danlos syndrome is associated with fatal cardiovascular complication s and intraoperative death. The lack of literature on cardiac surgery in th e syndrome makes it difficult for surgeons to assess the risk of an operati on and to choose optimal treatment. We describe the ease of a 63-year-old m an with Ehlers-Danlos syndrome type I or II, mitral regurgitation and atria l fibrillation who was managed successfully with mitral valve repair and su rgical cardioversion.