Arrhythmogenic right ventricular (RV) dysplasia consists of a dilatation of
the right ventricle with a reduction of RV ejection fraction with fibrofat
ty replacement of the RV myocardium in the face of a well-preserved left ve
ntricular systolic function. Arrhythmogenic RV dysplasia, which is a cause
of sudden unexpected death, has been reported from many geographic areas, i
ncluding the United States, Europe, and the Far East. This case report pres
ents the first case of arrhythmogenic RV dysplasia in an American Indian (N
ative American) patient.