Objective and Importance: Ganglioglioneurocytoma is not yet a well defined
clinical and histopathological entity; recent reports outline the histopath
ological features of this very rare trimorphous tumor, under different name
s with its basic components of gangliocytoma, neurocytoma and glioma. Four
previous reports described this tumor in eleven patients. This is the first
case report describing ganglioglioneurocytoma in the posterior fossa. Clin
ical Presentation and Intervention: A 31-year old male with midline posteri
or fossa ganglioglioneurocytoma is described, providing the neuroimages and
histopathological studies. Conclusion: Ganglioglioneurocytoma is a rare mi
xed neuronal and glial tumor that can also occur in the posterior fossa.