Childhood dermatitis herpetiformis (DH) is rare. The true prevalence and in
cidence of this condition are unknown. We report a 7-year-old boy presentin
g with nonpruritic inflammatory papules on the buttocks and extensor surfac
es, clinico-pathologically consistent with Sweet's neutrophilic dermatosis.
Immunofluorescence studies showed IgA deposits in the dermal papillae cons
istent with DH. Remission was achieved with a gluten-free diet and dapsone.
Childhood DH may present different clinical signs to the adult form and mi
sdiagnosis can occur if immunofluorescence is not requested on skin biopsy.