Brom's three-patch technique for repair of supravalvular aortic stenosis

Objective: Case histories of all patients (n = 29) operated on for supraval vular aortic stenosis from 1962 to the present were reviewed to study diffe rent techniques and outcomes, The technique of symmetric aortoplasty with 3 patches (1 in each sinus) is described and compared with other methods. Me thods: Case reports were reviewed and follow-up was completed by contacting the patient's (pediatric) cardiologist. We aimed for a last follow-up visi t, including Doppler echocardiographic studies, in a period no more than 12 months earlier than December 1997, Supravalvular aortic stenosis was discr ete in 25 and diffuse with involvement of the aortic arch and arch vessels in 4 patients. Additional anomalies were bicuspid aortic valve (n = 5), coa rctation (n = 3), ascending aortic aneurysm (n = 1), mitral valve insuffici ency (n = 2), pulmonary valvular stenosis (n = 1), and peripheral pulmonary artery stenosis (n = 2), Eleven patients had Williams syndrome and 1 patie nt had Noonan syndrome. Symmetric aortoplasty with 3 patches (1 in each sin us) was used in 13 patients, whereas other nonsymmetric methods (1, 2, or Y -shaped patches) were used in 16 patients. Mean follow-up was 10.5 years (r ange: 4 months-36 years), Results: All techniques adequately decreased the pressure gradient, Progression of preoperative aortic valve insufficiency o r de novo regurgitation was not observed except in 1 patient in whom the pa tches inserted were too large. Conclusions: No difference could be demonstr ated in outcome for any surgical technique; however, reconstruction of the aortic root with autologous pericardial patches in each sinus after transec tion of the aorta has the advantage of symmetry while restoring the normal aortic root anatomy.