Leiomvosarcoma involving the larynx is extremely rare and may be difficult
to diagnose. Likewise, because of the rarity of this lesion, little informa
tion exists with regard to long-term follow-up or optimal management. Repor
ted here is a review of the literature and a case report of a patient with
leiomyosarcoma of the larynx treated by surgery alone with 5 years of follo
w-up.