Malignant rhabdoid tumor of the vulva. Case report

The poor prognosis of malignant rhabdoid tumor is emphasized and histopatho logical criteria for distinction from epithelial sarcoma of the vulva are d iscussed. Immunohistochemical analyses were performed by using nine differe nt antigens including vimentin, cytokeratin, epithelial membrane antigen, c arcinoembryonic antigen, desmin, muscle-specific actin, S-100 protein, AP-1 5, neuron specific enolase. This is the sixth reported case of a malignant rhabdoid tumor of the vulva. The patient died eight months after the initia l diagnosis in spite of a combination of surgery, adjuvant chemotherapy and external radiotherapy.