We report a 9-year-old boy with a sinonasal ossifying fibroma, probably con
genital, with atypical findings on CT and MRT. CT revealed a soft-tissue de
nsity mass in the sphenoethmoidal sinuses, nasal cavity and right maxillary
sinus with a few foci of calcification and with remodelling and destructio
n of the adjacent facial bones. MRI showed high signal on T2- and intermedi
ate signal on T1-weighted images. A thin, partly enhancing outer shell and
some nonenhancing septa were visible on contrast-enhanced images. MRI also
showed the tumour to extend into the anterior cranial fossa. Subtotal remov
al was performed. We compare our findings with reports in the literature an
d discuss the differences from fibrous dysplasia.