An Ii-month-old Turkish female infant with Weaver syndrome together with at
rial septal defect and patent ductus arteriosus which was operated successf
ully is reported, Weaver syndrome is a very rare disorder of unknown etiolo
gy characterized by accelerated growth of prenatal onset, advanced osseous
maturation, special craniofacial features, umbilical hernia, and hoarse low
-pitched cry. Congenital cardiac defect is not a usual finding. The present
ed case is the first reported child with Weaver syndrome in the literature
operated for a congenital cardiac defect.