Monilethrix is a hereditary hair disorder that occurs monosymptomatically o
r as a monilethrix syndrome combined with other ectodermal anomalies. We re
port two siblings with the triple combination of monilethrix, keratosis pil
aris, and koilonychia. In one of our patients, the hair disorder improved,
with maximum hair growth up to 8 cm in length after her first menstrual per
iod occurred, suggesting that hormonal influences may improve the hair diso
rders in monilethrix.