Paratesticular desmoplastic small round cell tumor: Case report and reviewof the literature

Desmoplastic small round cell tumor (DSRCT) is a rare neoplasm mainly affec ting young males and typically located in the abdomen. Prognosis is general ly very poor. We report a rare case of paratesticular DSRCT in a 17-year-ol d boy, presenting with an isolated left scrotal mass. The patient had an ex cellent outcome after complete surgical resection of the tumor and adjuvant multi-agent chemotherapy. DSRCT should be included in the differential dia gnosis of small round cell tumors of the paratesticular region in adolescen ts and young adults. Tumor resection and chemotherapy may be beneficial for these patients. Our experience and a review of the literature suggest that DSRCT located in the paratesticular region may have a better prognosis tha n its more frequent abdominal counterpart. J. Surg. Oncol. 1999;71:269-272. (C) 1999 Wiley-Liss, Inc.